2024-11-1020200041-430110.24953/turkjped.2020.04.0212-s2.0-85089318838http://dx.doi.org/10.24953/turkjped.2020.04.021https://hdl.handle.net/20.500.14288/17030Background: Neuroglial choristomas are rare entities that are composed of differentiated neuroectodermal cells presenting where they do not belong. Case: Here in this paper, we represent a two-year old patient with a very rare presentation of neuroglial choristoma which manifested itself within a thyroglossal duct cyst. In this paper we will also discuss pathogenesis, clinical manifestation, differential diagnosis and management of the neuroglial choristomas. Conclusion: In conclusion we believe this unique case may aid in understanding the pathophysiology, differential diagnosis, and management of this rare congenital anomaly.PediatricsJournal Article559511900021Q47125