Publication:
Successful treatment with anakinra in generalized spiculated porokeratosis and severe hidradenitis suppurativa in a patient with MVK and MEFV mutations

dc.contributor.coauthorOktem, Ayse
dc.contributor.coauthorCavdarli, Busra
dc.contributor.coauthorBostanci, Seher
dc.contributor.coauthorHeper, Aylin
dc.contributor.departmentSchool of Medicine
dc.contributor.facultymemberYes
dc.contributor.kuauthorRasulova, Günel
dc.contributor.kuauthorVural, Seçil
dc.contributor.schoolcollegeinstituteSCHOOL OF MEDICINE
dc.date.accessioned2024-11-09T23:02:42Z
dc.date.issued2023
dc.description.abstractThe synergistic effect of two mutations of the innate immune system may facilitate hyperactivation and dysregulation of the inflammasome in skin macrophages. This case connects two diseases, hidradenitis suppurativa and porokeratosis, by the central role of autoinflammation.
dc.description.fulltextNo
dc.description.harvestedfromManual
dc.description.indexedbyScopus
dc.description.indexedbyPubMed
dc.description.indexedbyWOS
dc.description.openaccessYES
dc.description.peerreviewstatusPeer-Reviewed
dc.description.publisherscopeInternational
dc.description.readpublishN/A
dc.description.sponsoredbyTubitakEuN/A
dc.description.studentonlypublicationNo
dc.description.studentpublicationNo
dc.description.versionN/A
dc.identifier.WoSQuartileQ2
dc.identifier.doi10.1093/ced/llac023
dc.identifier.eissn1365-2230
dc.identifier.embargoN/A
dc.identifier.endpage165
dc.identifier.issn1365-2230
dc.identifier.issue2
dc.identifier.pubmed36730507
dc.identifier.scopus2-s2.0-85147319694
dc.identifier.startpage161
dc.identifier.urihttps://doi.org/10.1093/ced/llac023
dc.identifier.urihttps://hdl.handle.net/20.500.14288/8343
dc.identifier.volume48
dc.identifier.wos000953989300031
dc.keywordsHidradenitis suppurativa
dc.keywordsHumans
dc.keywordsInterleukin 1 receptor antagonist protein
dc.keywordsMutation
dc.keywordsPorokeratosis
dc.keywordsPyrin
dc.keywordsSkin
dc.keywordsInterleukin 1 receptor blocking agent
dc.keywordsComplication
dc.keywordsGenetics
dc.keywordsSuppurative hidradenitis
dc.language.isoeng
dc.publisherOxford University Press
dc.relation.affiliationKoç University
dc.relation.collectionKoç University Institutional Repository
dc.relation.ispartofClinical and experimental dermatology
dc.relation.openaccessN/A
dc.rightsN/A
dc.subjectMedicine
dc.titleSuccessful treatment with anakinra in generalized spiculated porokeratosis and severe hidradenitis suppurativa in a patient with MVK and MEFV mutations
dc.typeJournal Article
dspace.entity.typePublication
local.contributor.kuauthorVural, Seçil
local.contributor.kuauthorRasulova, Günel
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relation.isGoalOfPublication.latestForDiscoverya9786601-9431-4553-9a46-013bb366fb87
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