Heart transplantation in high risk arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVDC/C) patient with cerebrovascular event

Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) usually originates from right ventricle, has a prevalence 1 in 1000 and leading cause of death in people aged less than 35 years of age, also desmosome mutations and family history can be seen in this disease. We reviewed the literature and reported the high risk patient with arrhythmogenic right ventricular dysplasia/ cardiomyopathy (ARVD/C) with right cerebral infarction. He had T wave inversion in chest leads V1 to V4 and had premature ventricular complexes of left bundle branch block and left axis deviation, or right bundle branch block (RBB) had implantable cardioverter defibrillator (ICD) implantation and fulfilled the task force criteria for diagnosis of ARVD/C. He had a history of cerebrovascular event, an ischemic stroke and had a family history of ARVD/C. He was in NYHA Class III-IV while he admitted to our clinic and was receiving maximum medical treatment. He was listed as Status IA due to biventriculer heart failure and had final therapeutic option as an orthotopic heart transplantation.