Publication:
Adrenal cortex-sparing surgery for bilateral multiple pheochromocytomas in a patient with von hippel-lindau disease

dc.contributor.coauthorAcar, Ömer, Tefekli, Ahmet
dc.contributor.coauthorMusaoğlu, Ahmet
dc.contributor.coauthorRozanes, İzzet
dc.contributor.coauthorEmre, Ali
dc.contributor.departmentSchool of Medicine
dc.contributor.kuauthorEsen, Tarık
dc.contributor.schoolcollegeinstituteSCHOOL OF MEDICINE
dc.date.accessioned2024-11-09T23:27:43Z
dc.date.issued2012
dc.description.abstractPheochromocytomas can be a part of familial neoplastic syndromes, in which case they tend to be multiple and involve both adrenal glands. Therefore, sparing adrenocortical function represents a major concern while dealing with these hereditary lesions. Herein, we describe the clinical characteristics and the management strategy of a patient with von Hippel-Lindau (VHL) disease who had multiple, bilateral pheochromocytomas as well as bilateral renal masses, pancreatic masses, and a paracaval mass. Only a portion of the left adrenal gland has remained in situ after two consecutive open surgeries and a percutaneous radiofrequency ablation which have been performed to treat the various components of this syndrome. No adrenal or extra-adrenal pheochromocytoma recurrences have been detected during a follow-up period of more than 2 years. Pancreatic and adrenal functions were normal throughout the postoperative period and never necessitated any replacement therapy. Adrenal cortex-sparing surgery is a valid option for VHL disease patients who present with synchronous bilateral adrenal pheochromocytomas.
dc.description.indexedbyWOS
dc.description.indexedbyScopus
dc.description.indexedbyPubMed
dc.description.openaccessYES
dc.description.publisherscopeInternational
dc.description.sponsoredbyTubitakEuN/A
dc.description.volume2012
dc.identifier.doi10.1155/2012/659104
dc.identifier.eissn1687-9635
dc.identifier.issn1687-9627
dc.identifier.quartileN/A
dc.identifier.scopus2-s2.0-84926357270
dc.identifier.urihttps://doi.org/10.1155/2012/659104
dc.identifier.urihttps://hdl.handle.net/20.500.14288/11765
dc.identifier.wos215252100239
dc.keywordsRetroperitoneoscopic partial adrenalectomy
dc.keywordsAdrenocortical function
dc.keywordsClinical-experience
dc.keywordsFamilies
dc.keywordsCt
dc.language.isoeng
dc.publisherHindawi Ltd
dc.relation.ispartofCase Reports in Medicine
dc.subjectMedicine
dc.subjectGeneral
dc.subjectInternal
dc.titleAdrenal cortex-sparing surgery for bilateral multiple pheochromocytomas in a patient with von hippel-lindau disease
dc.typeJournal Article
dspace.entity.typePublication
local.contributor.kuauthorEsen, Tarık
local.publication.orgunit1SCHOOL OF MEDICINE
local.publication.orgunit2School of Medicine
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